SURGICAL TREATMENT OF AN ADVANCED STAGE THYMOMA IN A GOOD’S SYNDROME PATIENT – CASE REPORT

Authors

  • André Sena Department of Cardiothoracic surgery, Hospital de Santa Maria, Lisbon, Portugal
  • Ricardo Ferreira Department of Cardiothoracic surgery, Hospital de Santa Maria, Lisbon, Portugal
  • João Gonçalves Department of Cardiothoracic surgery, Hospital de Santa Maria, Lisbon, Portugal
  • Ângelo Nobre Department of Cardiothoracic surgery, Hospital de Santa Maria, Lisbon, Portugal

DOI:

https://doi.org/10.48729/pjctvs.89

Abstract

We report a rare case of an advanced stage thymoma with right superior pulmonary lobe, superior vena cava, innominate vein and pericardium invasion in a patient with Good’s syndrome. In a multidisciplinary discussion, surgical resection was deemed the best initial approach, since invaded structures could be safely managed. The tumor was fully resected and included partial resection of the superior pulmonary lobe, superior vena cava and innominate vein. The encircled right phrenic nerve was dissected from the tumor and preserved. The superior vena cava and innominate vein were reconstructed using autologous pericardium patch. Immunoglobulin replacement and radiotherapy were initiated afterwards. No signs of relapse at 6 months follow-up. In such advanced cases, aggressive surgical intervention should be considered as first line of treatment, as long as full resection can be anticipated, since complete resection is the leading factor for long-term prognosis.

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Published

25-04-2021

How to Cite

1.
Sena A, Ferreira R, Gonçalves J, Nobre Ângelo. SURGICAL TREATMENT OF AN ADVANCED STAGE THYMOMA IN A GOOD’S SYNDROME PATIENT – CASE REPORT. Rev Port Cir Cardiotorac Vasc [Internet]. 2021 Apr. 25 [cited 2022 Dec. 8];26(4):269-71. Available from: https://pjctvs.com/index.php/journal/article/view/89

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