• Isabel Armas General Surgery / Unidade Local de Saúde do Nordeste (ULSNE), Portugal
  • José Vidoedo Vascular Surgery / Centro Hospitalar Tâmega e Sousa (CHTS), Portugal
  • Luís Pedro Afonso Patology Department / Instituto Português de Oncologia do Porto (IPO Porto), Portugal
  • Augusto Moreira Surgical Oncology / Instituto Português de Oncologia do Porto (IPO Porto), Portugal
  • Joaquim Abreu de Sousa Surgical Oncology / Instituto Português de Oncologia do Porto (IPO Porto), Portugal




Ephitelioid Hemangioendothelioma (EHE) is a rare type of tumor with vascular and sarcomatous components. There's only another case published of an internal jugular vein (IJV) EHE. A case of a 50 years-old woman with a palpable and pulsatile mass on the left cervical area is reported. Doppler ultrasound and magnetic resonance imaging showed an IVJ' 4 cm mass. Cytology was inconclusive. Surgical treatment was therefore decided and during surgery a mass inside the left IJV, with local nonsuspicious lymph nodes, was confirmed. The mass was resected including a segmental resection of the IJV and one affected tributary vessel. Lymphadenectomy of the adjacent cervical levels was performed. Histologic examination depicted an EHE without metastatic lymph nodes. Tumor was staged as pT1bN0M0 and a multidisciplinary sarcoma group proposed surveillance. Patient remained well, without evidence of disease and without complications in a twenty-four months follow-up period.


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How to Cite

Armas I, Vidoedo J, Afonso LP, Moreira A, Abreu de Sousa J. EPITHELIOID HEMANGIOENDOTHELIOMA OF THE INTERNAL JUGULAR VEIN. Rev Port Cir Cardiotorac Vasc [Internet]. 2021 May 26 [cited 2023 Feb. 3];26(2):155157. Available from: https://pjctvs.com/index.php/journal/article/view/132



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