Surgical Repair Of Severe Mitral And Tricuspid Valve Regurgitation In Patient With Left Ventricle Noncompaction - A Case Report

Authors

  • Aayushi Donariya Department of Cardiovascular & Thoracic Surgery, U. N. Mehta Institute of Cardiology and Research Center, Civil Hospital Campus, Asarwa, Ahmedabad, Gujarat, India https://orcid.org/0009-0009-6348-7593
  • Herin Patel Department of Cardiovascular & Thoracic Surgery, U. N. Mehta Institute of Cardiology and Research Center, Civil Hospital Campus, Asarwa, Ahmedabad, Gujarat, India https://orcid.org/0009-0004-6629-5419
  • Fagun Gajjar Department of Cardiovascular & Thoracic Surgery, U. N. Mehta Institute of Cardiology and Research Center, Civil Hospital Campus, Asarwa, Ahmedabad, Gujarat, India
  • Shobhit Mathur Department of Cardiovascular & Thoracic Surgery, U. N. Mehta Institute of Cardiology and Research Center, Civil Hospital Campus, Asarwa, Ahmedabad, Gujarat, India https://orcid.org/0009-0005-8058-9875
  • Archit Patel Department of Cardiovascular & Thoracic Surgery, U. N. Mehta Institute of Cardiology and Research Center, Civil Hospital Campus, Asarwa, Ahmedabad, Gujarat, India
  • Kartik Patel Department of Cardiovascular & Thoracic Surgery, U. N. Mehta Institute of Cardiology and Research Center, Civil Hospital Campus, Asarwa, Ahmedabad, Gujarat, India https://orcid.org/0000-0003-1092-5034

DOI:

https://doi.org/10.48729/pjctvs.524

Keywords:

Cardiomyopathy, Left ventricular non-compaction, Mitral regurgitation

Abstract

Left ventricular non-compaction (LVNC) cardiomyopathy is a rare congenital cardiomyopathy which is characterized by prominent and extensive trabeculation and deep intertrabecular recesses communicating with left ventricular cavity. Here we present a rare case report of patient with severe secondary Mitral regurgitation (MR) and severe tricuspid regurgitation (TR) in LVNC cardiomyopathy who underwent MV Repair using ring annuloplasty with #28 CG future ring and kay’s suture annuloplasty for severe TR and its postoperative management. Patient recovered well after surgery and was discharged with improved hemodynamics. The valve surgery in patients with such cardiomyopathy is very rare. This case will add to the small growing literature of surgery in severe secondary Mitral regurgitation in LVNC and the problems we faced while coming off bypass and its postoperative management.

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References

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Published

04-08-2025

How to Cite

1.
Donariya A, Patel H, Gajjar F, Mathur S, Patel A, Patel K. Surgical Repair Of Severe Mitral And Tricuspid Valve Regurgitation In Patient With Left Ventricle Noncompaction - A Case Report. Rev Port Cir Cardiotorac Vasc [Internet]. 2025 Aug. 4 [cited 2025 Sep. 5];32(2):69-72. Available from: https://pjctvs.com/index.php/journal/article/view/524

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Clinical Cases

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