Large congenital pulmonary airway malformation with mucinous cell clusters – a case report

Authors

  • Tiago Magalhães Neonatal Intensive Care Unit, Neonatology Department, Centro Hospitalar Universitário de São João, Porto, Portugal; Faculty of Medicine of the University of Porto, Porto, Portugal
  • Rita Costa Faculty of Medicine of the University of Porto, Porto, Portugal; Departmentof Cardiothoracic Surgery, Centro Hospitalar Universitário de São João, Porto, Portugal
  • Gustavo Rocha Neonatal Intensive Care Unit, Neonatology Department, Centro Hospitalar Universitário de São João, Porto, Portugal
  • Elson Salgueiro Faculty of Medicine of the University of Porto, Porto, Portugal; Departmentof Cardiothoracic Surgery, Centro Hospitalar Universitário de São João, Porto, Portugal
  • Henrique Soares Neonatal Intensive Care Unit, Neonatology Department, Centro Hospitalar Universitário de São João, Porto, Portugal; Faculty of Medicine of the University of Porto, Porto, Portugal

DOI:

https://doi.org/10.48729/pjctvs.182

Abstract

We report the clinical case of a 38 weeks gestational age neonate, antenatally diagnosed with a left large macrocystic pulmonary malformation conditioning dextrocardia. At birth, he presented with respiratory distress requiring non-invasive ventilation with high-flow nasal cannula (HFNC). A left inferior lobectomy was performed via thoracotomy on day 21 of life. Histological features of the lesion were compatible with congenital pulmonary airway malformation (CPAM) type I with muci- nous cell clusters. No surgical complications were reported and the neonate was discharged six days after surgery. Follow-up two months after surgery was unremarkable.

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References

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Published

03-07-2022

How to Cite

1.
Magalhães T, Costa R, Rocha G, Salgueiro E, Soares H. Large congenital pulmonary airway malformation with mucinous cell clusters – a case report. Rev Port Cir Cardiotorac Vasc [Internet]. 2022 Jul. 3 [cited 2022 Sep. 27];29(2):67-9. Available from: https://pjctvs.com/index.php/journal/article/view/182

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Clinical Cases

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