@article{Graça_Almeida Cunha_Lopes_Carvalho_Prieto_2022, place={Lisbon, Portugal}, title={Thoracic Epithelioid Hemangioendothelioma: clinical demonstration and therapeutic procedures}, volume={29}, url={https://pjctvs.com/index.php/journal/article/view/276}, DOI={10.48729/pjctvs.276}, abstractNote={<div class="page" title="Page 1"> <div class="layoutArea"> <div class="column"> <p>Epithelioid hemangioendotheliomais a low to intermediate grade malignant vascular tumors that can involve any organ. About 60-80%of patients are women, patient ages range 7 to 81 years, with a median age of 38 years. Four cases of thoracic epithelioid hemangioendotheliomas with different clinical presentation and disease progression are reported. Cases 1 and 2 are pulmonary epithelioid hemangioendotheliomas diagnosed at different advanced stages and patients died after 6 and 2,5 months of medical treatment, respectively. Case 3 corresponds to pleural epithelioid hemangioendothelioma, submit- ted to left lung decortication and pleuro-pericardial window; patient is free either from symptoms and radiographic manifestations for 10 months of follow-up. Case 4, of mediastinal epithelioid hemangioendothelioma, represented by a mass in the upper left mediastinum adherent to the aortic arch; patient underwent block excision of the mass followed by chemotherapy; subsequent recurrence 41 months later and the patient died 8 months after. The reported 4 cases reveal the heterogeneous clinical presentation of epithelioid hemangioendotheliomas with behavior in between benign and high-grade tumors, raising difficulty in either differentiating from other vascular tumors and previewing clinical outcome.</p> </div> </div> </div>}, number={2}, journal={Portuguese Journal of Cardiac Thoracic and Vascular Surgery}, author={Graça, Luís Lourenço and Almeida Cunha, Sara and Lopes, Rita Susana and Carvalho, Lina and Prieto, David}, year={2022}, month={Jul.}, pages={39–44} }