A Rare Case of Pulmonary Artery Sarcoma





Pulmonary artery sarcoma (PAS) is a rare and aggressive mesenchymal tumor with an overall poor prognosis1-5. Due to similar clinical and radiologic findings, PAS is often misdiagnosed as a pulmonary embolism (PE) frequently leading to prolonged anticoagulation therapy, which delays the correct diagnosis 1-3. By presenting this clinical case our objective is to emphasize characteristic CT findings that favour a neoplastic origin of a pulmonary intravascular filling defect. PET-CT and MRI have also an important potential role in its diagnosis and therapeutical management.


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von Falck C, Meyer B, Fegbeutel C et al. Imaging features of primary Sarcomas of the great vessels in CT, MRI and PET/CT: a single-center experience. BMC Med Imaging. 2013; 13,25. doi: 10.1186/1471-2342-13-25.

Liu MX, Ma ZH, Jiang T et al. Differential Diagnosis of Pulmonary Artery Sarcoma and Central Chronic Pulmonary Thromboembolism Using CT and MR Images. Heart Lung Circ. 2018, Jul,27(7):819-827. doi: 10.1016/j.hlc.2017.06.716.

Gan, HL, ZhangJQ, ZhouQW et al. Surgical treatment of pulmonary artery sarcoma. J Thorac Cardiovasc Surg. 2011;142:1469-72. doi: 10.1016/j.jtcvs.2011.03.013.

Fujii Y, Koizumi J, Hara T et al. Endovascular Catheter Biopsy for the Diagnosis of Pulmonary Artery Sarcoma. Ann Vasc Dis. 2019; Jun 25;12(2):256-259. doi: 10.3400/avd.hdi.19-00001.




How to Cite

Brazão Carvalho V, Roque Almeida J, Leal C. A Rare Case of Pulmonary Artery Sarcoma. Rev Port Cir Cardiotorac Vasc [Internet]. 2024 Feb. 9 [cited 2024 Jun. 13];30(4):71-3. Available from: https://pjctvs.com/index.php/journal/article/view/369



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