Giant Intrathoracic Desmoid Tumor – a Case Report

Authors

  • Sara Cunha Department of Cardiothoracic Surgery, Coimbra University and Hospital Centre, Portugal https://orcid.org/0000-0002-9756-1837
  • Luis L. Graça Department of Cardiothoracic Surgery, Coimbra University and Hospital Centre, Portugal https://orcid.org/0000-0003-3077-1618
  • Rita Lopes Department of Cardiothoracic Surgery, Coimbra University and Hospital Centre, Portugal https://orcid.org/0000-0001-7808-293X
  • Vânia Almeida Department of Cardiothoracic Surgery, Coimbra University and Hospital Centre, Portugal https://orcid.org/0000-0002-2202-7402
  • Rita Pancas Department of Cardiothoracic Surgery, Coimbra University and Hospital Centre, Portugal

DOI:

https://doi.org/10.48729/pjctvs.326

Keywords:

Desmoid Tumors, Desmoid Fibromatosis, Thoracic Surgery

Abstract

Desmoid tumors are soft tissue neoplasms arising from fascial and muscle-aponeurotic structure. These tumors are locally aggressive and have a high recurrence rate, even after complete resection. We present the case of a female with a giant intrathoracic desmoid tumor. She underwent complete surgical resection with no disease recurrence. Desmoid tumors’ natural history is not well defined and is often enigmatic, making these tumors difficult to manage. Currently, for intrathoracic desmoid tumors, medical treatment is the recommended approach, nevertheless, surgery can be considered in selected patients.

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References

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Published

09-02-2024

How to Cite

1.
Cunha S, L. Graça L, Lopes R, Almeida V, Pancas R. Giant Intrathoracic Desmoid Tumor – a Case Report . Rev Port Cir Cardiotorac Vasc [Internet]. 2024 Feb. 9 [cited 2024 Jun. 14];30(4):63-6. Available from: https://pjctvs.com/index.php/journal/article/view/326

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Clinical Cases

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